Pentalogy of Cantrell Cantrell pentalojisi

Ectopia cordis is a rare malformation presenting as an isolated lesion or as part of the Cantrell’s pentalogy syndrome characterized by midline closure defects. A preterm male baby who did not have antenatal follow-up was born by caesarean section with evisceration of the heart and major parts of the intraabdominal organs. Combination of these findings suggested the diagnosis of Cantrell’s pentalogy. Despite intensive care, the patient died soon after the birth due to the poor clinical state. In order to make contribution to literature about this subject, this rare case of neonate with Cantrell’s pentalogy was reported. Antenatal diagnosis, appropriate antenatal care and delivery in a hospital that is capable for treatment is important for a better prognosis.